中国医学科学院学报

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中国医学科学院学报

中国医学科学院学报 ›› 2013, Vol. 35 ›› Issue (2): 136-139.doi: 10.3881/j.issn.1000-503X.2013.02.002

• 论著 • 上一篇    下一篇

结节性硬化症伴发肝肾血管平滑肌脂肪瘤的CT表现

李跃兴1,向军益1,李洁1,丁建平1,林上奇2   

  1. 1杭州师范大学 附属医院放射科,杭州3100152杭州市红十字会医院放射科,杭州310015
  • 收稿日期:2012-08-15 出版日期:2013-05-03 发布日期:2013-05-03
  • 通讯作者: 李跃兴 电话:13616543955,电子邮件:liyuexingxing@163.com E-mail:liyuexingxing@163.com

CT Findings of Tuberous Sclerosis Associated with Hepatic and Renal Angiomyolipomas

LI Yue-xing1, XIANG Jun-yi1, LI Jie1, DING Jian-ping1, LIN Shang-qi2   

  1. 1 Department of Radiology, the Affiliated Hospital of Hangzhou Normal University, Hangzhou 310015, China 2 Department of Radiology, Hangzhou Red Cross Hospital, Hangzhou 310015, China
  • Received:2012-08-15 Online:2013-05-03 Published:2013-05-03
  • Contact: LI Yue-xing Tel:13616543955,E-mail:liyuexingxing@163.com E-mail:liyuexingxing@163.com

摘要: 目的 描述结节性硬化症伴发的肝、肾血管平滑肌脂肪瘤的CT表现,并分析二者的相关性。方法 回顾性分析7例经临床及影像学检查确诊的结节性硬化症的CT表现。结果 颅脑CT显示侧脑室室管膜下钙化结节和/或非钙化结节6例;腹部CT显示双肾血管平滑肌脂肪瘤7例,其中2例同时伴发肝血管平滑肌脂肪瘤;胸部CT显示淋巴管肌瘤病1例。结论 结节性硬化症的肝、肾血管平滑肌脂肪瘤具有典型的影像学特征,并且肝血管平滑肌脂肪瘤与双肾血管平滑肌脂肪瘤具有相关性,影像学检查具有重要的价值和临床意义。

关键词: 结节性硬化症, 血管平滑肌脂肪瘤, CT

Abstract: Objective To summarize the clinical and computed tomographic(CT) findings of tuberous sclerosis(TS) associated with hepatic and renal angiomyolipomas. Method We retrospectively analyzed the clinical and CT findings of 7 TS patients with hepatic and renal angiomyolipomas. Results Brain CT showed calcified nodules and/or the uncalcified nodule in the lateral ventricle subependymal in 7 patients.Abdominal CT showed bilateral renal angiomyolipomas in 7 cases and hepatic angiomyolipomas in 2 cases. Chest CT showed lymphangioleiomyomatosis in one case. Conclusions TS associated with merger hepatic and/or renal angiomyolipomas have typical CT findings. Liver angiomyolipomas shows certain correlation with bilateral renal angiomyolipomas.

Key words: tuberous sclerosis, angiomyolipomas, computed tomography